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KMID : 1035220150070020085
Korean Journal of Neuromuscular Disorders
2015 Volume.7 No. 2 p.85 ~ p.88
Posterior Reversible Encephalopathy Syndrome after Steroid Pulse Therapy in Juvenile Dermatomyositis
Choi Byung-Woo

Oh Seong-Il
Oh Kyung-Pil
Oh Ki-Wook
Abstract
Posterior reversible encephalopathy syndrome (PRES) is a clinic-radiological diagnosis characterized by seizures, headaches, lethargy, confusion, visual disturbances, and transient magnetic resonance imaging changes in the posterior circulation distribution. Juvenile dermatomyositis (JDM) is a rare but serious systemic autoimmune myopathy. We report a 17-year-old women with dermatomyositis who developed PRES after usual intravenous methylprednisolone treatment.
KEYWORD
Posterior reversible encephalopathy syndrome, Juvenile dermatomyositis, Drug pulse therapy
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