KMID : 1035220150070020085
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Korean Journal of Neuromuscular Disorders 2015 Volume.7 No. 2 p.85 ~ p.88
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Posterior Reversible Encephalopathy Syndrome after Steroid Pulse Therapy in Juvenile Dermatomyositis
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Choi Byung-Woo
Oh Seong-Il Oh Kyung-Pil Oh Ki-Wook
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Abstract
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Posterior reversible encephalopathy syndrome (PRES) is a clinic-radiological diagnosis characterized by seizures, headaches, lethargy, confusion, visual disturbances, and transient magnetic resonance imaging changes in the posterior circulation distribution. Juvenile dermatomyositis (JDM) is a rare but serious systemic autoimmune myopathy. We report a 17-year-old women with dermatomyositis who developed PRES after usual intravenous methylprednisolone treatment.
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KEYWORD
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Posterior reversible encephalopathy syndrome, Juvenile dermatomyositis, Drug pulse therapy
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